Table 2 (A) Aortic diameter and aortic dilatation rate by MRI. (B) Non-cardiovascular Marfan features
| Â | Aortic diametersa | Aortic diameter changeb |
|---|---|---|
A | ||
Aortic dimension by MRI | ||
Aortic root (mm) | 45 ± 5.6 | 1.23 ± 2.10 |
Ascending aorta (mm) | 29 ± 3.9 | 0.84 ± 1.39 |
Aortic arch (mm) | 24 ± 3.1 | 0.57 ± 1.47 |
Proximal descending aorta (mm) | 24 ± 3.5 | 0.53 ± 1.54 |
Distal descending aorta (mm) | 21 ± 3.1 | 0.81 ± 1.57 |
Diaphragm (mm) | 21 ± 3.2 | 0.33 ± 1.21 |
Bifurcation | 16 ± 3.6 | 0.46 ± 1.83 |
Marfan features | Â | Marfan features | Â |
|---|---|---|---|
B | |||
Ectopia Lentis | 88 (46%) | Dural ectasia | 98 (52%) |
Myopia | 37 (19%) | Protrusio | 5 (3%) |
Flat cornea | 15 (8%) | Increased height-span ratio | 37 (19%) |
Increased axial eye-length | 25 (13%) | Scoliosis | 50 (26%) |
Hypoplastic iris | 17 (9%) | Reduced elbow extension | 25 (13%) |
Thumb/wrist signs | 83 (44%) | Facial features | 56 (29%) |
Pectus carinatum | 66 (35%) | Striae | 128 (67%) |
Pectus excavatum | 29 (15%) | Joint problems | 48 (25%) |
Hindfoot deformity | 56 (29%) | Arched palate | 119 (63%) |
Pes planus | 83 (44%) | Mitral valve prolapse | 104 (55%) |
Pneumothorax | 28 (15%) | Â | Â |